Cystic Fibrosis in Children: Comprehensive Nursing Notes
Cystic Fibrosis in Children: Comprehensive Nursing Notes ( 12 Questions)
The client asks, "Why does CF lead to the production of thick mucus in the lungs and other organs?" Which of the following responses by the nurse is accurate?
The CFTR gene mutation does not cause excessive water transport in the body. In fact, CF leads to a defect in chloride and water transport in cells, which results in the production of thick mucus.
CF does not result in an overproduction of a specific enzyme that thickens mucus. Instead, it affects the functioning of the CFTR protein, which is responsible for maintaining the balance of chloride and water in cells.
CF does not primarily affect the production of surfactant in the lungs. Surfactant is a substance that helps prevent the collapse of alveoli in the lungs, and CF primarily affects the mucus and airway clearance, not surfactant production.
"The CFTR gene mutation impairs chloride and water transport in cells.”.
Choice A rationale:
The CFTR gene mutation does not cause excessive water transport in the body.
In fact, CF leads to a defect in chloride and water transport in cells, which results in the production of thick mucus.
Choice B rationale:
CF does not result in an overproduction of a specific enzyme that thickens mucus.
Instead, it affects the functioning of the CFTR protein, which is responsible for maintaining the balance of chloride and water in cells.
Choice D rationale:
CF does not primarily affect the production of surfactant in the lungs.
Surfactant is a substance that helps prevent the collapse of alveoli in the lungs, and CF primarily affects the mucus and airway clearance, not surfactant production.